Raghib Syndrome
Raghib syndrome is a rare cardiac anomaly that was originally described by raghib et al.
Raghib syndrome. Raghib syndrome is a rare developmental complex. Although few cases have been reported in the literature there are a number of techniques to redirect the lsvc flow to the right atrium. Coronary sinus ostial atresia. Ccsd accounts for less than 1 of asd and 0 1 of all congenital heart diseases chds.
Raghib syndrome is a rare congenital defect classically consisting of a persistent left superior vena cava plsvc and an unroofed coronary sinus cs 1 1. Surgery is classically considered definitive treatment 2 2. It has also been associated with other congenital malformations including ventricular septal defects enlargement of the tricuspid annulus and pulmonary stenosis. In 1965 as a developmental complex consisting of termination of the left superior vena cava in the left atrium absence of the coronary sinus and an atrial septal defect commonly located at the posterior inferior angle of the atrial septum.
Raghib s syndrome is characterized by the combination of abnormal drainage from the left superior vena cava into the left atrium the presence of an atrial septal defect and the absence of a coronary sinus. 22q11 2 distal deletion syndrome. Raghib syndrome is a rare developmental complex which consists of persistence of the left superior vena cava plsvc along with coronary sinus ostial atresia and atrial septal defect. Persistence of the left superior vena cava.
This raghib complex anomaly has also been associated with other congenital malformations including ventricular septal defects enlargement of the tricuspid annulus and pulmonary stenosis. Raghib syndrome is a special type of asd which is known as coronary sinus spetal defect ccsd first described by raghib 1. Comprehensive guides on hundreds of diseases and conditions from mayo clinic experts.